| CASE REPORT |
|
| Year : 2011 | Volume
: 27
| Issue : 4 | Page : 550-552 |
|
|
Successful anesthetic management of a child with blepharophimosis syndrome and atrial septal defect for reconstructive ocular surgery
Dalim Kumar Baidya, Puneet Khanna, Anil Kumar, Dilip Shende
Department of Anaesthesia and Intensive Care, All India Institute of Medical Sciences, New Delhi, India
Correspondence Address:
Dalim Kumar Baidya
Department of Anesthesia and Intensive Care, All India Institute of Medical Sciences, 8/67, Gent's Hostel, New Delhi - 110 029
India
 Source of Support: None, Conflict of Interest: None  | Check |
DOI: 10.4103/0970-9185.86607
|
|
|
Blepharophimosis syndrome is an autosomal dominant disorder characterized by eyelid malformation, involvement of reproductive system and abnormal facial morphology leading to difficult airway. We report a rare association of blepharophimosis syndrome and atrial septal defect in a 10-year-old girl who came for reconstruction surgery of eyelid. The child had dyspnea on exertion. Atrial septal defect was identified preoperatively by clinical examination and echocardiography. Anesthesia management was complicated by failure in laryngeal mask airway placement and Cobra perilaryngeal airway was subsequently used. |
|
|
|
| [FULL TEXT] [PDF]* |
|
 |
|
